What is ICD-10 code G71.0340?

G71.0340 is the ICD-10-CM diagnosis code for Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by sarcoglycan protein dysfunction, but the specific type of sarcoglycan affected is not specified. G71.0340 is a billable code, meaning it can be reported on a claim as a primary or secondary diagnosis when supported by documentation. G71.0340 is part of the FY2026 ICD-10-CM code set published by the CMS National Center for Health Statistics and used on Medicare, Medicaid, and commercial claims in the United States.

Is G71.0340 billable?

Yes. G71.0340 is a billable ICD-10-CM code that can be reported on professional and institutional claims as a primary or secondary diagnosis when the provider documentation supports the specific condition described. Billable codes in ICD-10-CM are coded to the highest level of specificity available for the documented diagnosis. G71.0340 is current for fiscal year 2026 and remains in the active CMS ICD-10-CM code set published by the National Center for Health Statistics.

What is the V28 vs V24 difference for G71.0340?

CMS phased in the V28 risk adjustment model over payment years 2024 (33%), 2025 (67%), and 2026 (100%), replacing V24. V28 consolidates HCC categories, removes some lower-acuity conditions, and recalibrates RAF weights across the entire model. For G71.0340, V28 maps to Muscular Dystrophy at RAF 0.000 while V24 mapped to Muscular Dystrophy at RAF 0.358. Both models can still appear in legacy data and in payer-specific lookback periods.

What should coders know when reporting G71.0340?

Use this code only when sarcoglycan dysfunction is confirmed but the specific subtype cannot be determined Encourage providers to obtain genetic testing to identify the specific sarcoglycan type for more precise coding Because G71.0340 maps to a payment HCC, the documentation must also satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's risk adjustment score.

G71.0340 ICD-10 Code: Limb girdle muscular

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

Code lookupG71.0340Effective periodFY2026 Apr Update (Apr 1-Sep 30)

FY 2026 Apr update / Diseases of the nervous system (G00-G99) / Diseases of myoneural junction and muscle (G70-G73)

G71.0340

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified

A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by sarcoglycan protein dysfunction, but the specific type of sarcoglycan affected is not specified.

Buddy Insight

CMS-HCC V28

Mapped

HCC 197

Muscular Dystrophy

RAF 0.0

CMS-HCC V24

Mapped

HCC 76

Muscular Dystrophy

RAF 0.358

ACA/HHS

Not risk-adjusted for this model/period.

RAF 0

ESRD/PACE

Mapped

HCC 76

Muscular Dystrophy

RAF 0.0

RXHCC

Not risk-adjusted for this model/period.

RAF 0

Code Trumping

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Code Book Path

Official

G71.03Limb girdle muscular dystrophies

G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction

G71.0340Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified

Inclusion Terms

Official

Sarcoglycanopathy, NOS

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for G71.0340 in this effective period.

Related Child Codes

Official

G71.0341Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction

G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

G71.0349Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

Includes

Official

ICD-10-CM does not list Includes notes for G71.0340 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for G71.0340 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for G71.0340 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for G71.0340 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for G71.0340 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance

Muscle biopsy or genetic testing confirming sarcoglycan protein deficiency

Clinical presentation: progressive proximal weakness, elevated creatine kinase

Documentation that the specific sarcoglycan subtype (alpha, beta, gamma, delta) could not be determined

Cardiac evaluation results (sarcoglycanopathies can cause cardiomyopathy)

MEAT Support

HCC Buddy guidance

Muscle biopsy or genetic testing confirming sarcoglycan protein deficiency

Clinical presentation: progressive proximal weakness, elevated creatine kinase

Documentation that the specific sarcoglycan subtype (alpha, beta, gamma, delta) could not be determined

Cardiac evaluation results (sarcoglycanopathies can cause cardiomyopathy)

Audit Caution

HCC Buddy guidance

Using this unspecified sarcoglycan code when genetic testing has identified the specific subtype

Not pursuing genetic subtyping, which affects prognosis and potential therapeutic options

Confusing sarcoglycanopathy with dystrophinopathy due to overlapping clinical severity

Failing to also code cardiac complications (cardiomyopathy) when present

Common Mistakes

HCC Buddy guidance

G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction should be used when the alpha subtype is confirmed

G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction should be used when the beta subtype is confirmed

G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction is for gamma, delta, or epsilon subtypes

G71.01 — Duchenne or Becker muscular dystrophy may have similar severity but involves dystrophin, not sarcoglycan

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is G71.0340 an HCC code?

Yes. G71.0340 maps to Muscular Dystrophy under the CMS-HCC V28 risk adjustment model (and Muscular Dystrophy under V24).

HCC Category Mapping

V28HCC 197, Muscular Dystrophy

0.000

V24HCC 76, Muscular Dystrophy

0.358

ESRDHCC 76, Muscular Dystrophy

0.000

RAF weights shown are the community, non-dual, aged base weights from the CMS risk adjustment model file. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

MEAT Criteria for G71.0340

For G71.0340to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
EEvaluate: test results, medication response, or physical findings reviewed by the provider
AAssess: explicit mention in the assessment or plan with acknowledgment of status
TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed G71.0340 during that encounter, not just copy-forwarded from a problem list.

What This Code Means

G71.0340 is the ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by sarcoglycan protein dysfunction, but the specific type of sarcoglycan affected is not specified. G71.0340 sits in the ICD-10-CM chapter for diseases of the nervous system (g00-g99), within the section covering diseases of myoneural junction and muscle (g70-g73).

Under the CMS-HCC V28 risk adjustment model, G71.0340 maps to Muscular Dystrophy (HCC 197) with a community, non-dual, aged base RAF weight of 0.000. Under the older V24 model, G71.0340 mapped to the same category but with a base RAF weight of 0.358, V28 recalibrated weights across the entire model. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

Use this code only when sarcoglycan dysfunction is confirmed but the specific subtype cannot be determined. Because G71.0340 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for G71.0340 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

•Use this code only when sarcoglycan dysfunction is confirmed but the specific subtype cannot be determined
•Encourage providers to obtain genetic testing to identify the specific sarcoglycan type for more precise coding

Clinical Significance

Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified represents a group of autosomal recessive muscular dystrophies caused by deficiency of sarcoglycan proteins, which form part of the dystrophin-associated glycoprotein complex. These sarcoglycanopathies can be clinically severe, sometimes mimicking Duchenne muscular dystrophy. Proper coding supports genetic subtyping efforts and treatment planning.

Documentation Requirements

✓Muscle biopsy or genetic testing confirming sarcoglycan protein deficiency
✓Clinical presentation: progressive proximal weakness, elevated creatine kinase
✓Documentation that the specific sarcoglycan subtype (alpha, beta, gamma, delta) could not be determined
✓Cardiac evaluation results (sarcoglycanopathies can cause cardiomyopathy)
✓Functional status and disease progression
✓Provider's explicit diagnosis of sarcoglycan-related limb girdle muscular dystrophy

Commonly Confused Codes

•G71.0341 — Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction should be used when the alpha subtype is confirmed
•G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction should be used when the beta subtype is confirmed
•G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction is for gamma, delta, or epsilon subtypes
•G71.01 — Duchenne or Becker muscular dystrophy may have similar severity but involves dystrophin, not sarcoglycan